Congenital total lipodystrophy and peripheral pulmonary artery stenosis
نویسندگان
چکیده
منابع مشابه
Congenital Stenosis of the Pulmonary Artery Branches.
CONGENITAL stenosis of the pulmonary artery branches is an anomaly characterized by narrowed segments of one or more of the main or peripheral branches of the pulmonary artery. Such conditions lhave been variously labeled pulmonary coaretation,' peripheral pulmonary stenosis,2 and multiple peripheral stenoses 3 of the pulmonary artery. Several cases of this anomaly have appeared in the literatu...
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Case 1 involved a 4-month-old intact male Somali cat in which peripheral pulmonary artery stenosis (PPS) was recognized after a cardiac murmur remained following patent ductus arteriosus ligation. Case 2, which involved a 1-year-old neutered male Norwegian Forest cat, and Case 3, which involved a 6-month-old intact female American Curl cat, were referred, because of cardiac murmurs. Grades III ...
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DS, a 21-year-old woman admitted to the hospital because of dyspnea and pleuritic chest pain for 5 days, had the diagnosis of congenital right PA stenosis since age 6 years, when a systolic precordial murmur was noted. Cardiac catheterization in childhood showed isolated mild right PA stenosis; the mean pressure in the pulmonary trunk was 30 mm Hg, and the mean right PA pressure was 15 mm Hg. S...
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Peripheral pulmonary artery stenosis is a rare form of congenital heart disease frequently associated with Williams and Alagille syndromes. Patients with this disease typically have systemic level right ventricular pressures secondary to obstruction at the lobar, segmental, and subsegmental branches. The current management of patients with peripheral pulmonary artery stenosis remains somewhat c...
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Selective right pulmonary arteriography and 3-dimensional computed tomography revealed multiple severe stenoses of the peripheral pulmonary artery associated with poststenotic aneurysms in a 65-year-old woman. She was referred to the hospital for evaluation of dry cough, gradually increasing dyspnea and multiple nodular shadows on a chest radiograph. Echocardiography and cardiac catheterization...
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ژورنال
عنوان ژورنال: Archives of Disease in Childhood
سال: 1997
ISSN: 0003-9888,1468-2044
DOI: 10.1136/adc.77.5.463f